Successful general anesthesia for cervical spine fusion in a patient with spondyloepiphyseal dysplasia congenita: A case report

Park, Sookyoung; Kang, Sung Hee; Joo, Sun Young; Cho, Eun Jung; Nam, Jinwoo

Case Report

Pediatric Anesthesia

Anesthesia and Pain Medicine 2011;6(3):294-297.
Published online July 30, 2011.

Successful general anesthesia for cervical spine fusion in a patient with spondyloepiphyseal dysplasia congenita: A case report

Sookyoung Park, Sung Hee Kang, Sun Young Joo, Eun Jung Cho, Jinwoo Nam

¹Department of Anesthesiology and Pain Medicine, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea. gkjw2000@yahoo.co.kr
²Department of Orthopedic Surgery, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea.

Abstract

Spondyloepiphyseal dysplasia congenita (SEDC) is a kind of skeletal dysplasia, inheritable condition. The clinical features of SEDC are dwarfism, myopia with or without retinal detachment, coxa vara, thoracic dysplasia with respiratory failure and laryngotracheal stenosis. A point of particular concern to anesthetists is odontoid hypoplasia which, combined with ligamentous laxity, leads to atlantoaxial instability. We report successful general anesthesia for cervical spine fusion of a patient with SEDC.

Key Words: Atlantoaxial instability, Spondyloepiphyseal dysplasia congenita